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Cellosaurus AT4BR (CVCL_ZT63)

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Cell line name AT4BR
Synonyms Ataxia Telangiectasia 4 BRighton
Accession CVCL_ZT63
Resource Identification Initiative To cite this cell line use: AT4BR (RRID:CVCL_ZT63)
Comments Derived from site: In situ; Skin; UBERON=UBERON_0002097.
Cell type: Fibroblast of skin; CL=CL_0002620.
Disease Ataxia telangiectasia syndrome (NCIt: C2887)
Ataxia telangiectasia (ORDO: Orphanet_100)
Species of origin Homo sapiens (Human) (NCBI Taxonomy: 9606)
Originate from same individual CVCL_ZT64 ! AT4BR LCL
Sex of cell Male
Age at sampling 8Y
Category Finite cell line
Publications

PubMed=7836839; DOI=10.1080/09553009414551951
Jane Cole, Colin Francis Arlett;
Cloning efficiency and spontaneous mutant frequency in circulating T-lymphocytes in ataxia-telangiectasia patients.
Int. J. Radiat. Biol. 66:S123-S131(1994)

PubMed=8794843; DOI=10.1080/095530096145139
Anthony R.M. Sproston, John Michael Boyle, Jim Heighway, Jillian M. Birch, David Scott;
Fibroblasts from Li-Fraumeni patients are resistant to low dose-rate irradiation.
Int. J. Radiat. Biol. 70:145-150(1996)

Cross-references
Encyclopedic resources Wikidata; Q98125507
Entry history
Entry creation02-Jul-2020
Last entry update30-Jan-2024
Version number6