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Cellosaurus AT3ABR (CVCL_M912)

[Text version]
Cell line name AT3ABR
Synonyms Ataxia Telangiectasia 3 Australia BRisbane
Accession CVCL_M912
Resource Identification Initiative To cite this cell line use: AT3ABR (RRID:CVCL_M912)
Comments From: Queensland Institute of Medical Research; Brisbane; Australia.
Transformant: NCBI_TaxID; 10376; Epstein-Barr virus (EBV).
Derived from site: In situ; Peripheral blood; UBERON=UBERON_0000178.
Sequence variations
Disease Ataxia telangiectasia syndrome (NCIt: C2887)
Ataxia telangiectasia (ORDO: Orphanet_100)
Species of origin Homo sapiens (Human) (NCBI Taxonomy: 9606)
Sex of cell Sex unspecified
Age at sampling Age unspecified
Category Transformed cell line
Publications

PubMed=7433105; DOI=10.1093/nar/8.16.3709; PMCID=PMC324185
Jane Houldsworth, Martin Francis Lavin;
Effect of ionizing radiation on DNA synthesis in ataxia telangiectasia cells.
Nucleic Acids Res. 8:3709-3720(1980)

PubMed=6197197; DOI=10.1016/0009-2797(83)90167-9
F. Paula Imray, Cheviot Kidson;
Responses of Huntington's disease and ataxia telangiectasia lymphoblastoid cells to bleomycin.
Chem. Biol. Interact. 47:325-336(1983)

PubMed=6228733; DOI=10.1016/0167-8817(83)90030-5
F. Paula Imray, Cheviot Kidson;
Perturbations of cell-cycle progression in gamma-irradiated ataxia telangiectasia and Huntington's disease cells detected by DNA flow cytometric analysis.
Mutat. Res. 112:369-382(1983)

PubMed=6504056; DOI=10.1016/0027-5107(84)90149-0
Philip Chen, F. Paula Imray, Cheviot Kidson;
Gene dosage and complementation analysis of ataxia telangiectasia lymphoblastoid cell lines assayed by induced chromosome aberrations.
Mutat. Res. 129:165-172(1984)

PubMed=2825700; DOI=10.1016/0006-291X(87)91629-9
Rahmah Mohamed, Surinder Pal Singh, Sharad Kumar, Martin Francis Lavin;
A defect in DNA topoisomerase II activity in ataxia-telangiectasia cells.
Biochem. Biophys. Res. Commun. 149:233-238(1987)

PubMed=2836804; DOI=10.1093/nar/16.9.3919; PMCID=PMC336565
Surinder Pal Singh, Rahmah Mohamed, C. Salmond, Martin Francis Lavin;
Reduced DNA topoisomerase II activity in ataxia-telangiectasia cells.
Nucleic Acids Res. 16:3919-3929(1988)

PubMed=8808599; PMCID=PMC1914811
Jocyndra Wright, Sharon Teraoka, Suna Onengut, Aslihan Tolun, Richard A. Gatti, Hans D. Ochs, Patrick Concannon;
A high frequency of distinct ATM gene mutations in ataxia-telangiectasia.
Am. J. Hum. Genet. 59:839-846(1996)

PubMed=9150358; DOI=10.1038/sj.onc.1201037
Dianne Watters, Kum Kum Khanna, Heather J. Beamish, Geoffrey W. Birrell, Kevin Spring, Padmini Kedar, Magtouf Gatei, Deborah Stenzel, Karen Hobson, Sergei V. Kozlov, Ning Zhang ...Show all 15 authors... , Aine Farrell, Jonathan Ramsay, Richard A. Gatti, Martin Francis Lavin; Show fewer authors
Cellular localisation of the ataxia-telangiectasia (ATM) gene product and discrimination between mutated and normal forms.
Oncogene 14:1911-1921(1997)

PubMed=9168117; DOI=10.1038/387520a0
Timothy Shafman, Kum Kum Khanna, Padmini Kedar, Kevin Spring, Sergei V. Kozlov, Timothy J. Yen, Karen Hobson, Magtouf Gatei, Ning Zhang, Dianne Watters, Mark Egerton ...Show all 15 authors... , Yosef Shiloh, Surender Kharbanda, Donald William Kufe, Martin Francis Lavin; Show fewer authors
Interaction between ATM protein and c-Abl in response to DNA damage.
Nature 387:520-523(1997)

PubMed=11080496; DOI=10.1074/jbc.M006190200
Nuri Gueven, Katherine E. Keating, Philip Chen, Toshiyuki Fukao, Kum Kum Khanna, Dianne Watters, Peter H. Rodemann, Martin Francis Lavin;
Epidermal growth factor sensitizes cells to ionizing radiation by down-regulating protein mutated in ataxia-telangiectasia.
J. Biol. Chem. 276:8884-8891(2001)

Cross-references
Encyclopedic resources Wikidata; Q54750911
Experimental variables resources EFO; EFO_0022451
Entry history
Entry creation05-Nov-2013
Last entry update19-Dec-2024
Version number19