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Cellosaurus Lu Rob 2 (CVCL_F0FY)

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Cell line name Lu Rob 2
Accession CVCL_F0FY
Resource Identification Initiative To cite this cell line use: Lu Rob 2 (RRID:CVCL_F0FY)
Comments Caution: The cell line is indicated by PubMed=2722184 to originate from the same patient as Lu-Rob (Cellosaurus=CVCL_3010) but no name is given, just the initials "L.R". We have thus named it Lu Rob 2 as we could not find any ATCC document indicating its name.
Derived from site: In situ; Skin; UBERON=UBERON_0002097.
Cell type: Fibroblast of skin; CL=CL_0002620.
Disease Ehlers-Danlos syndrome, type IV (NCIt: C125699)
Vascular Ehlers-Danlos syndrome (ORDO: Orphanet_286)
Species of origin Homo sapiens (Human) (NCBI Taxonomy: 9606)
Originate from same individual CVCL_3010 ! Lu Rob
Sex of cell Female
Age at sampling 50Y
Category Finite cell line
Publications

PubMed=3337712; DOI=10.1016/0006-291x(88)90497-4
Andrea Superti-Furga, Beat Steinmann;
Impaired secretion of type III procollagen in Ehlers-Danlos syndrome type IV fibroblasts: correction of the defect by incubation at reduced temperature and demonstration of subtle alterations in the triple-helical region of the molecule.
Biochem. Biophys. Res. Commun. 150:140-147(1988)

PubMed=2722184; DOI=10.1007/BF00284038
Andrea Superti-Furga, Beat Steinmann, Francesco Ramirez, Peter H. Byers;
Molecular defects of type III procollagen in Ehlers-Danlos syndrome type IV.
Hum. Genet. 82:104-108(1989)

Cross-references
Cell line collections (Providers) ATCC; CRL-1384 - Discontinued
Entry history
Entry creation14-Aug-2025
Last entry update14-Aug-2025
Version number1