ID   Dbt-MYCN/indP3F
AC   CVCL_C7HL
DR   Wikidata; Q117704283
RX   PubMed=28138962;
CC   Characteristics: Transduced with a retroviral construct expressing MYCN constitutively and a doxycycline-inducible PAX3-FOXO1 lentiviral expression construct (PubMed=28138962).
CC   Genetic integration: Method=Transduction; Gene=HGNC; HGNC:3819; FOXO1 (Note=PAX3-FOXO1 fusion).
CC   Genetic integration: Method=Transduction; Gene=HGNC; HGNC:7559; MYCN.
CC   Genetic integration: Method=Transduction; Gene=HGNC; HGNC:8617; PAX3 (Note=PAX3-FOXO1 fusion).
CC   Genetic integration: Method=Transduction; Gene=HGNC; HGNC:11730; TERT.
CC   Genetic integration: Method=Transduction; Gene=MGI; MGI:88174; Bmi1.
CC   Genetic integration: Method=Transduction; Gene=UniProtKB; P00557; Escherichia coli hygromycin-B 4-O-kinase (hph) (HygR).
CC   Genetic integration: Method=Transduction; Gene=UniProtKB; P13249; S.alboniger pac (PuroR).
CC   Derived from site: In situ; Skeletal muscle; UBERON=UBERON_0001134.
CC   Cell type: Muscle satellite cell; CL=CL_0000594.
DI   NCIt; C75482; Duchenne muscular dystrophy
DI   ORDO; Orphanet_98896; Duchenne muscular dystrophy
OX   NCBI_TaxID=9606; ! Homo sapiens (Human)
HI   CVCL_C7HJ ! Dbt
SX   Male
AG   7Y
CA   Telomerase immortalized cell line
DT   Created: 21-03-23; Last updated: 10-04-25; Version: 6
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RX   PubMed=28138962; DOI=10.1002/path.4867; PMCID=PMC5357165;
RA   Pandey P.R., Chatterjee B., Olanich M.E., Khan J., Miettinen M.M.,
RA   Hewitt S.M., Barr F.G.;
RT   "PAX3-FOXO1 is essential for tumour initiation and maintenance but not
RT   recurrence in a human myoblast model of rhabdomyosarcoma.";
RL   J. Pathol. 241:626-637(2017).
//